An accessory labioscrotal fold associated with anorectal malformation in female neonates

The association of perineal lipomas with anorectal malformations in the newborn has been reported previously (Shaul DB, Monforte HL, Pena A, et al. Surgical management of perineal masses in patients with anorectal malformations. J Pediatr Surg 2005;40:188-191; Wester T, Rintala RJ. Perineal lipomas associated with anorectal malformations. Pediatr Surg Int 2006;22:979-981). Only 2 cases of accessory labioscrotal fold with perineal lipoma have been reported (Redman JF, Ick KA, North PE. Perineal lipoma and an accessory labial fold in a female neonate. J Urol 2001;166:1450, Sule JD, Skoog SJ, Tank ES. Perineal lipoma and the accessory labioscrotal fold: an etiologic relationship. J Urol 1994;151:475-477). To our knowledge, no other reports of accessory labioscrotal fold with anorectal malformation in the female patient have appeared in the literature. We present our experience of treatment with these rare cases and a review of the literature.