Fronto-orbito-sphenoidal fibrous dysplasia

Eight patients with fronto-orbito-sphenoidal fibrous dysplasia, aged between 9 and 37 years, half of them male, were radically or nearly radically excised with immediate autogenous bone graft reconstruction. They had had frontal bulging and proptosis on the affected sides for 3 to 20 years. Four had decreased vision on the diseased side, and among them 1 had corneal ulceration due to proptosis and lower lid intropion. Optic nerve decompression was used with the other 3 patients who had narrowed optic canals. Cosmetic improvement was achieved after surgery. The vision of the normal and blind eyes was not changed after optic nerve decompression. The progression of visual loss stopped after surgery. One eye with decreased vision improved after optic nerve decompression.