Abstract
We report a case of idiopathic lymphoplasmacellular mucositis (ILPM) of the vulva in a 48-year-old woman with partial interferon-γ receptor 1 (IFN-γR1) deficiency. The lesion had an unusual ulcerovegetative presentation. Remarkable response was observed with oral and topical steroids in the first 3 weeks. However, the lesion recurred after tapering oral steroids and continuous low-dose oral steroids were required to suppress recurrence. To the best of our knowledge, this is the first case report of ILPM in a patient with partial IFN-γR1 deficiency. ILPM should be included in the differential diagnosis of persistent vulvar ulcerovegetative lesions.
Original language | English |
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Pages (from-to) | 50-52 |
Number of pages | 3 |
Journal | Dermatologica Sinica |
Volume | 37 |
Issue number | 1 |
DOIs | |
State | Published - 01 2019 |
Externally published | Yes |
Bibliographical note
Publisher Copyright:© 2019 Dermatologica Sinica | Published by Wolters Kluwer - Medknow.
Keywords
- Idiopathic lymphoplasmacellular mucositis
- interferon-receptor 1 deficiency
- vulva