Macrophage Activation Syndrome as Initial Presentation of Systemic Lupus Erythematosus

Say Tin Yeap; Jiunn Ming Sheen; Ho Chang Kuo; Kao Pin Hwang; Kuender D. Yang; Hong Ren Yu

doi:10.1016/S1875-9572(08)60010-8

Macrophage Activation Syndrome as Initial Presentation of Systemic Lupus Erythematosus

Say Tin Yeap, Jiunn Ming Sheen, Ho Chang Kuo, Kao Pin Hwang, Kuender D. Yang, Hong Ren Yu^*

^*Corresponding author for this work

Chang Gung Memorial Hospital

Research output: Contribution to journal › Journal Article › peer-review

15 Scopus citations

Abstract

Macrophage activation syndrome (MAS) is known to be a severe and potentially life-threatening complication of rheumatic disorder, especially systemic juvenile rheumatoid arthritis. It is very rare for MAS to be an initial presentation of systemic lupus erythematosus (SLE). Here, we report a 14-year-old girl in whom MAS developed as an initial presentation of SLE. With early diagnosis and administration of cyclosporine A, she had a fair outcome. Further testing showed positive anti-dsDNA about 8 months later.

Original language	English
Pages (from-to)	39-42
Number of pages	4
Journal	Pediatrics and Neonatology
Volume	49
Issue number	2
DOIs	https://doi.org/10.1016/S1875-9572(08)60010-8
State	Published - 04 2008
Externally published	Yes

Keywords

cyclosporine A
macrophage activation syndrome
systemic lupus erythematosus
type V hyperlipo-proteinemia

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10.1016/S1875-9572(08)60010-8

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title = "Macrophage Activation Syndrome as Initial Presentation of Systemic Lupus Erythematosus",

abstract = "Macrophage activation syndrome (MAS) is known to be a severe and potentially life-threatening complication of rheumatic disorder, especially systemic juvenile rheumatoid arthritis. It is very rare for MAS to be an initial presentation of systemic lupus erythematosus (SLE). Here, we report a 14-year-old girl in whom MAS developed as an initial presentation of SLE. With early diagnosis and administration of cyclosporine A, she had a fair outcome. Further testing showed positive anti-dsDNA about 8 months later.",

keywords = "cyclosporine A, macrophage activation syndrome, systemic lupus erythematosus, type V hyperlipo-proteinemia",

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T1 - Macrophage Activation Syndrome as Initial Presentation of Systemic Lupus Erythematosus

AU - Yeap, Say Tin

AU - Sheen, Jiunn Ming

AU - Kuo, Ho Chang

AU - Hwang, Kao Pin

AU - Yang, Kuender D.

AU - Yu, Hong Ren

PY - 2008/4

Y1 - 2008/4

N2 - Macrophage activation syndrome (MAS) is known to be a severe and potentially life-threatening complication of rheumatic disorder, especially systemic juvenile rheumatoid arthritis. It is very rare for MAS to be an initial presentation of systemic lupus erythematosus (SLE). Here, we report a 14-year-old girl in whom MAS developed as an initial presentation of SLE. With early diagnosis and administration of cyclosporine A, she had a fair outcome. Further testing showed positive anti-dsDNA about 8 months later.

AB - Macrophage activation syndrome (MAS) is known to be a severe and potentially life-threatening complication of rheumatic disorder, especially systemic juvenile rheumatoid arthritis. It is very rare for MAS to be an initial presentation of systemic lupus erythematosus (SLE). Here, we report a 14-year-old girl in whom MAS developed as an initial presentation of SLE. With early diagnosis and administration of cyclosporine A, she had a fair outcome. Further testing showed positive anti-dsDNA about 8 months later.

KW - cyclosporine A

KW - macrophage activation syndrome

KW - systemic lupus erythematosus

KW - type V hyperlipo-proteinemia

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SP - 39

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JO - Pediatrics and Neonatology

JF - Pediatrics and Neonatology

IS - 2

ER -

Macrophage Activation Syndrome as Initial Presentation of Systemic Lupus Erythematosus

Abstract

Keywords

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