Macrophage Activation Syndrome as Initial Presentation of Systemic Lupus Erythematosus

Say Tin Yeap; Jiunn Ming Sheen; Ho Chang Kuo; Kao Pin Hwang; Kuender D. Yang; Hong Ren Yu

doi:10.1016/S1875-9572(08)60010-8

Macrophage Activation Syndrome as Initial Presentation of Systemic Lupus Erythematosus

Say Tin Yeap
, Jiunn Ming Sheen
, Ho Chang Kuo
, Kao Pin Hwang
, Kuender D. Yang
, Hong Ren Yu^*

^*Corresponding author for this work

Chang Gung Memorial Hospital

Research output: Contribution to journal › Journal Article › peer-review

16 Scopus citations

Abstract

Macrophage activation syndrome (MAS) is known to be a severe and potentially life-threatening complication of rheumatic disorder, especially systemic juvenile rheumatoid arthritis. It is very rare for MAS to be an initial presentation of systemic lupus erythematosus (SLE). Here, we report a 14-year-old girl in whom MAS developed as an initial presentation of SLE. With early diagnosis and administration of cyclosporine A, she had a fair outcome. Further testing showed positive anti-dsDNA about 8 months later.

Original language	English
Pages (from-to)	39-42
Number of pages	4
Journal	Pediatrics and Neonatology
Volume	49
Issue number	2
DOIs	https://doi.org/10.1016/S1875-9572(08)60010-8
State	Published - 04 2008
Externally published	Yes

Keywords

cyclosporine A
macrophage activation syndrome
systemic lupus erythematosus
type V hyperlipo-proteinemia

Access to Document

10.1016/S1875-9572(08)60010-8

Cite this

@article{fc0e0252599846f49d75477c3fe97f1a,

title = "Macrophage Activation Syndrome as Initial Presentation of Systemic Lupus Erythematosus",

abstract = "Macrophage activation syndrome (MAS) is known to be a severe and potentially life-threatening complication of rheumatic disorder, especially systemic juvenile rheumatoid arthritis. It is very rare for MAS to be an initial presentation of systemic lupus erythematosus (SLE). Here, we report a 14-year-old girl in whom MAS developed as an initial presentation of SLE. With early diagnosis and administration of cyclosporine A, she had a fair outcome. Further testing showed positive anti-dsDNA about 8 months later.",

keywords = "cyclosporine A, macrophage activation syndrome, systemic lupus erythematosus, type V hyperlipo-proteinemia",

author = "Yeap, \{Say Tin\} and Sheen, \{Jiunn Ming\} and Kuo, \{Ho Chang\} and Hwang, \{Kao Pin\} and Yang, \{Kuender D.\} and Yu, \{Hong Ren\}",

year = "2008",

month = apr,

doi = "10.1016/S1875-9572(08)60010-8",

language = "英语",

volume = "49",

pages = "39--42",

journal = "Pediatrics and Neonatology",

issn = "1875-9572",

publisher = "Elsevier (Singapore) Pte Ltd",

number = "2",

}

TY - JOUR

T1 - Macrophage Activation Syndrome as Initial Presentation of Systemic Lupus Erythematosus

AU - Yeap, Say Tin

AU - Sheen, Jiunn Ming

AU - Kuo, Ho Chang

AU - Hwang, Kao Pin

AU - Yang, Kuender D.

AU - Yu, Hong Ren

PY - 2008/4

Y1 - 2008/4

N2 - Macrophage activation syndrome (MAS) is known to be a severe and potentially life-threatening complication of rheumatic disorder, especially systemic juvenile rheumatoid arthritis. It is very rare for MAS to be an initial presentation of systemic lupus erythematosus (SLE). Here, we report a 14-year-old girl in whom MAS developed as an initial presentation of SLE. With early diagnosis and administration of cyclosporine A, she had a fair outcome. Further testing showed positive anti-dsDNA about 8 months later.

AB - Macrophage activation syndrome (MAS) is known to be a severe and potentially life-threatening complication of rheumatic disorder, especially systemic juvenile rheumatoid arthritis. It is very rare for MAS to be an initial presentation of systemic lupus erythematosus (SLE). Here, we report a 14-year-old girl in whom MAS developed as an initial presentation of SLE. With early diagnosis and administration of cyclosporine A, she had a fair outcome. Further testing showed positive anti-dsDNA about 8 months later.

KW - cyclosporine A

KW - macrophage activation syndrome

KW - systemic lupus erythematosus

KW - type V hyperlipo-proteinemia

UR - https://www.scopus.com/pages/publications/54149112343

U2 - 10.1016/S1875-9572(08)60010-8

DO - 10.1016/S1875-9572(08)60010-8

M3 - 文章

C2 - 18947015

AN - SCOPUS:54149112343

SN - 1875-9572

VL - 49

SP - 39

EP - 42

JO - Pediatrics and Neonatology

JF - Pediatrics and Neonatology

IS - 2

ER -

Macrophage Activation Syndrome as Initial Presentation of Systemic Lupus Erythematosus

Abstract

Keywords

Access to Document

Other files and links

Fingerprint

Cite this