Marfan syndrome with myocarditis demonstrated by99Tcm-HMPAO-labelled wbc and201T1 scintigraphy: Report of three cases in a chinese family

Tzu Chen Yen*, Shih Hwa Yeh

*Corresponding author for this work

Research output: Contribution to journalJournal Article peer-review

3 Scopus citations

Abstract

Marfan syndrome is a heritable disorder of connectivc tissue in which the most prominent abnormalities occur in the ocular J cardiovascular and skeletal systems. Although cardiovascular complications are infrequent in patients under 20 years of age, whenever they do occur, they are the major cause of death. Here we report three cases in a Chinese family with clinical evidence of myocarditis associated with Marfan syndrome. The99Tcm-hexamethylpropyleneamine oxime (HMPAO)-labelled white blood cell and201T1 single photon emission computed tomographic heart scans show indications of an inflammatory process involving the myocardium. After comparison with the pathology results, the accuracy of these studies is seen to be 100%. We thus introduce these simple methods to evaluate myocardial viability in patients with Marfan syndrome.

Original languageEnglish
Pages (from-to)712-716
Number of pages5
JournalNuclear Medicine Communications
Volume14
Issue number8
DOIs
StatePublished - 08 1993
Externally publishedYes

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