Primitive Neuroectodermal Tumor of the Lingual Nerve: A Case Report

　　　　　本文報告一位5歲女童罹患由舌神經起源之原始神經外胚層上皮瘤（primitive neuroectodermal tumor）。經過外科手術及化學治療1年以後，病人伋然存活，無任何復發或 轉移的現象。此腫瘤很少發生於小孩的頭頸部，同時這也是文獻中第1例由小兒顱神經長出 的原始神經外胚層上皮瘤。由於此腫瘤的預後相當差，外科和內科的治療都必須要很積極。 我們強調在診斷小兒頭頸部腫瘤時，應把原始神經外胚層上皮瘤列入鑑別診斷之一。
　　　　　This is a report of a primitive neuroectodermal tumor (PNET) arising from the lingual nerve of a 5-year-old girl. Twelve months after surgical excision and postoperative chemotherapy, the patient remained alive without any evidence of recurrence or metastasis. The occurrence of PNET in the head and neck region in children is rare. This is the first case report in the literature of a PNET originating from a cranial nerve in a child. Because of its aggressive nature and poor prognosis, aggressive surgical and medical treatment regimens are needed. Surgeons should be mindful to include PNET in the differential diagnosis of head and neck tumors.