Pulmonary lymphangioleiomyomatosis followed by a localized retroperitoneal lymphangioleiomyoma: Case report

Hui Chun Tai, Jui Wei Lin, Yi Hsi Wang, Hock Liew Eng, Hung I. Lu, Yueh Wei Liu, Chao Cheng Huang*

*Corresponding author for this work

Research output: Contribution to journalJournal Article peer-review

3 Scopus citations

Abstract

Lymphangioleiomyomatosis is a rare disease that affects females of reproductive age. Microscopically, it is characterized by abnormal proliferation of immature smooth muscle-like cells that grow diffusely in the lung. Extrapulmonary manifestations in the mediastinum, peritoneum and pelvic lymph nodes are uncommon. We here describe a patient who initially presented with pulmonary lymphangioleiomyomatosis and subsequently developed a localized retroperitoneal mass. Pathologic examination showed that the mass was a lymphangioleiomyoma. The result of the immunohistochemical study was the same as that for the pulmonary lesion. It is therefore suggested that metastatic lymphangioleiomyoma should be included in the differential diagnosis in the patient with pulmonary lymphangioleiomyomatosis presenting with an extrapulmonary lesion.

Original languageEnglish
Pages (from-to)821-824
Number of pages4
JournalAPMIS
Volume114
Issue number11
DOIs
StatePublished - 11 2006

Keywords

  • Lung
  • Lymphangioleiomyomatosis
  • Metastasis
  • Retroperitoneum

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