摘要
Hunter syndrome (mucopolysaccharidosis, type II; MPS II) is one of a
heterogeneous group of recessively inherited mucopolysaccharide storage diseases.
Patients with mucopolysaccharidosis show progressive involvement and derangement
of many organs, especially upper airway anomalies, which are the major cause of
perioperative death. In recent years, a CO2 laser is often applied to upper airway
lesions. A 16-year-old patient suffering from Hunter syndrome was scheduled for
CO2 laser surgery because of sleep apnea and respiratory stridor. Otolarygological
examination revealed bulging of the bilateral false cord with stenosis of the glottis.
We adopted sevoflurane mask induction and high-frequency jet ventilation to
overcome the perioperative airway problems. The anesthetic course was uneventful,
and the patient was discharged 2 days after the operation.
原文 | 美式英語 |
---|---|
頁(從 - 到) | 614-618 |
期刊 | 長庚醫學 |
卷 | 23 |
發行號 | 10 |
出版狀態 | 已出版 - 2000 |
Keywords
- 高頻噴射換氣
- 黏多醣